Bushke's Syndrome - Ollendorf

Buschke's syndrome - Ollendorf (s. Buschke - Ollendorf), disseminated dermatofibrosis with osteopoikilia ^[1] . It was first described by the German dermatologist Abraham Buschke and the American physician Helen Ollendorf Kurt ^[2] in 1928. The Bushke – Ollendorf syndrome is inherited in an autosomal dominant manner ^[3] .

Family-hereditary constitutional anomaly of the middle germinal leaf. On the skin in the upper part of the back, abdomen, nape, shoulders, hips, lumbosacral region, a rash appears, located symmetrically, light yellow in color, of a dense consistency, slightly rising above the skin.

Radiologically, against the background of an almost normal bone in the cancellous substance of the epiphyses and metaphyses of long tubular bones, metatarsal and metacarpal bones, phalanges, spotted foci of obscuration are observed. Less commonly affected are vertebrae, ribs, sternum, skull. Sometimes the disease is combined with blue sclera syndrome, imperfect bone formation, debility , epilepsy .