Syndrome of left heart hypoplasia (GLOS) or hypoplasia of the left heart ( English Hypoplastic left heart syndrome ) is a clinical syndrome characterized by the presence of congenital heart defects such as moderate or severe hypoplasia or atresia of the mitral valve , left ventricle, aortic valve and various degree of hypoplasia of the ascending aorta .
| Hypoplasia syndrome of the left heart | |
|---|---|
| ICD-10 | Q 23.4 |
| ICD-10-KM | |
| ICD-9 | 746.7 |
| ICD-9-KM | |
| Omim | 241550 |
| Diseasesdb | 31507 |
| Medlineplus | 001106 |
| eMedicine | ped / 1131 |
| Mesh | C14.240.400.625 |
Since systemic ejection depends entirely on the right ventricle through the open arterial duct (OAI) into the aorta , patients die due to the closure of OAA in the first days or weeks of life [3] .
Frequency
According to the National Birth Defect Prevention Network , birth defects occur in about three percent of babies born alive in the United States. Among these defects, CVD occurs on average in one of 4,344 newborns, which makes a total of about 960 newborns every year in the United States [4] [5] [6] .
Notes
- ↑ Disease Ontology release 2019-05-13 - 2019-05-13 - 2019.
- ↑ Monarch Disease Ontology release 2018-06-29sonu - 2018-06-29 - 2018.
- ↑ Julien IE Hoffman, Samuel Kaplan, Richard R. Liberthson Prevalence of congenital heart disease American Heart Journal 2004 Mar; 147 (3) : 425-39. PMID 14999190
- ↑ CDC - Congenital Heart Defects, Facts about Hypoplastic Left Heart Syndrome - NCBDDD
- ↑ CDC Data & Statistics | Feature: Updated Estimates for Selected Birth Defects Archived March 4, 2016.
- ↑ Parker SE, Mai CT, Canfield MA, Rickard R., Wang Y., Meyer RE, Anderson P., Mason CA, Collins JS, Kirby RS, Correa A; National Birth Defects Prevention Network. Updated National Birth Prevalence estimates for selected birth defects in the United States, 2004-2006. (Eng.) // Birth Defects Res A Clin Mol Teratol. : journal. - 2010 .-- Vol. 88 , no. 12 . - P. 1008-1016 . - DOI : 10.1002 / bdra.20735 . - PMID 20878909 .
Links
- HLHS Information Page Questions to ask medical professionals and insurance company, plus resources
- Hypoplastic Left Heart Syndrome information from Seattle Children's Hospital Heart Center
- Card-AG , The Cardiologycal Working Group of the University Pediatric Clinic Munster
- Hypoplastic Left Heart Syndrome , American Heart Association
- Overview at Cincinnati Children's Hospital Medical Center
- Overview at University of Michigan Congenital Heart Center
- Cardiac Center at The Children's Hospital of Philadelphia
- Hypoplastic left heart syndrome information for parents.
- Little Hearts Matter, a charity providing support and information on HLHS and other single ventricle heart defects
- Baby hearts press
- www.congenitalheartdefects.com
- 120+ stories of children born with Hypoplastic Left Heart Syndrome hosted by the The Congenital Heart Information Network .
- HLHS email support groups / discussion list hosted by the The Congenital Heart Information Network (membership required).
- Little Hearts , Inc. - Providing hope with stories of children with HLHS and other CHDs. Email support group (membership required)
- HeartLine , a charity for children with heart conditions and their families
- Designer Heart , A Congenital Heart Defect Network.
- It's My Heart , a non-profit organization created to provide support to and advocating for those affected by Acquired and Congenital Heart Defects.