Limited scleroderma is a sub-form of systemic scleroderma [1] . It is also abbreviated as CREST syndrome. The first five letters are the names of the diseases that accompany the limited form.
- 'C' - Calcinosis - from English. calcinosis
- 'R' - ' Raynaud's disease - from English. Raynaud's phenomenon
- 'E' - Esophagitis - from English. esophageal dysmotility
- 'S' - Sclerodactyly - from English sclerodactyly
- 'T' - Teleangiectasia - from English telangiectasias
| Limited scleroderma | |
|---|---|
 CREST syndrome (calcification and sclerodactyly) | |
| ICD-10 | M 34.1 |
| ICD-10-KM | |
| ICD-9 | 710.1 |
| Omim | 181750 |
| DiseasesDB | 29764 |
| Mesh | D017675 |
It is a form of systemic scleroderma associated with antibodies to centromeres , and usually extends to the kidneys. If the lungs are involved in the process, then this manifests itself in the form of pulmonary arterial hypertension .
Notes
- ↑ Winterbauer RH Multiple telangiectasia, Raynaud'S phenomenon, sclerodactyly, and subcutanious calcinosis: a syndrome mimicking hereditary hemorrhagic telangiectasia (English) // The Johns Hopkins Medical Journal : journal. - 1964. - Vol. 114 . - P. 361-383 . - PMID 14171636 .